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Breadcrumb Francesco Saverio Tedesco Tedesco lab Stem Cells and Neuromuscular Regeneration Laboratory : Publications Lab contentLab contentIn this section Overview Members Vacancies Publications PublicationsCrick/Pre-Crick (-)Pre-Crick publications (23) Facet Crick/Pre-Crick Publications Displaying 1 - 20 of 23Last updated : 23 April 2024 03:38 Investigating the role of dystrophin isoform deficiency in motor function in Duchenne muscular dystrophy Authors (19) Mary Chesshyre Deborah Ridout Yasumasa Hashimoto Yoko Ookubo Silvia Torelli Kate Maresh[...] Mariacristina Scoto Giovanni Baranello Adnan Manzur Yoshitsugu Aoki Francesco Muntoni Journal of Cachexia, Sarcopenia and Muscle Published 1 April 2022 Crick labsFrancesco Saverio TedescoFull details Dystrophin deficiency affects human astrocyte properties and response to damage Authors (10) Jenny Lange Olivia Gillham Reem Alkharji Simon Eaton Giulia Ferrari Monika Madej Michael FlowerFrancesco Saverio Tedesco Francesco Muntoni Patrizia Ferretti Glia Published 1 March 2022 Crick labsFrancesco Saverio TedescoFull details The non-muscle ADF/cofilin-1 controls sarcomeric actin filament integrity and force production in striated muscle laminopathies Authors (22) Nicolas Vignier Maria Chatzifrangkeskou Luca Pinton Hugo Wioland Thibaut Marais Mégane Lemaitre[...] Guillaume Romet-Lemonne Howard J WormanFrancesco Saverio Tedesco Antoine Jégou Antoine Muchir Cell Reports Published 24 August 2021 Crick labsFrancesco Saverio TedescoFull details Generation of two genomic-integration-free DMD iPSC lines with mutations affecting all dystrophin isoforms and potentially amenable to exon-skipping Authors (3) Giulia Ferrari Francesco MuntoniFrancesco Saverio Tedesco Stem Cell Research Published 1 March 2020 Crick labsFrancesco Saverio TedescoFull details Challenging the "chromatin hypothesis" of cardiac laminopathies with LMNA mutant iPS cells Authors (2) Chiara MozzettaFrancesco Saverio Tedesco The Journal of Cell Biology Published 2 September 2019 Crick labsFrancesco Saverio TedescoFull details Pericytes in muscular dystrophies Authors (3) Louise Anne MoyleFrancesco Saverio Tedesco Sara Benedetti Advances in Experimental Medicine and Biology Published 31 May 2019 Crick labsFrancesco Saverio TedescoFull details Stem cell culture conditions and stability: a joint workshop of the PluriMes Consortium and Pluripotent Stem Cell Platform Authors (20) Glyn N Stacey Peter W Andrews Ivana Barbaric Charlotta Boiers Amit Chandra Giulio Cossu[...] Valentin P Shichkin Alison R StaceyFrancesco Saverio Tedesco Oliver Thompson Ravenska Wagey Regenerative Medicine Published 2 April 2019 Crick labsFrancesco Saverio TedescoFull details Combined Notch and PDGF signaling enhances migration and expression of stem cell markers while inducing perivascular cell features in muscle satellite cells Authors (14) Mattia Francesco Maria Gerli Louise Anne Moyle Sara Benedetti Giulia Ferrari Ekin Ucuncu Martina Ragazzi[...] Pierpaolo Ala Paolo De Coppi Shahragim Tajbakhsh Giulio CossuFrancesco Saverio Tedesco Stem Cell Reports Published 5 March 2019 Crick labsFrancesco Saverio TedescoFull details Modeling skeletal muscle laminopathies using human induced pluripotent stem cells carrying pathogenic LMNA mutations Authors (7) Heather B Steele-Stallard Luca Pinton Shilpita Sarcar Tanel Ozdemir Sara M Maffioletti Peter S ZammitFrancesco Saverio Tedesco Frontiers in Physiology Published 15 October 2018 Crick labsFrancesco Saverio TedescoFull details Efficient CRISPR/Cas9-mediated editing of trinucleotide repeat expansion in myotonic dystrophy patient-derived iPS and myogenic cells Authors (23) Sumitava Dastidar Simon Ardui Kshitiz Singh Debanjana Majumdar Nisha Nair Yanfang Fu[...]Francesco Saverio Tedesco Joris R Vermeesch J Keith Joung Marinee K Chuah Thierry VandenDriessche Nucleic Acids Research Published 19 September 2018 Crick labsFrancesco Saverio TedescoFull details Book review Authors (1)Francesco Saverio Tedesco Neuromuscular Disorders Published 1 March 2018 Crick labsFrancesco Saverio TedescoFull details Reversible immortalisation enables genetic correction of human muscle progenitors and engineering of next-generation human artificial chromosomes for Duchenne muscular dystrophy Authors (21) Sara Benedetti Narumi Uno Hidetoshi Hoshiya Martina Ragazzi Giulia Ferrari Yasuhiro Kazuki[...] George Dickson Graziella Messina Mitsuo Oshimura Giulio CossuFrancesco Saverio Tedesco EMBO Molecular Medicine Published 1 February 2018 Crick labsFrancesco Saverio TedescoFull details Enhanced energetic state and protection from oxidative stress in human myoblasts overexpressing BMI1 Authors (12) Silvia Dibenedetto Maria Niklison-Chirou Claudia P Cabrera Matthew Ellis Lesley G Robson Paul Knopp[...] Martina Ragazzi Valentina Di Foggia Michael R Barnes Aleksandar Radunovic Silvia Marino Stem Cell Reports Published 8 August 2017 Crick labsFrancesco Saverio TedescoFull details Muscle interstitial cells: A brief field guide to non-satellite cell populations in skeletal muscle Authors (3)Francesco Saverio Tedesco Louise A Moyle Eusebio Perdiguero Methods in Molecular Biology Published 1 March 2017 Crick labsFrancesco Saverio TedescoFull details Ret function in muscle stem cells points to tyrosine kinase inhibitor therapy for facioscapulohumeral muscular dystrophy Authors (9) Louise A Moyle Eric Blanc Oihane Jaka Johanna Prueller Christopher RS BanerjiFrancesco Saverio Tedesco Stephen DR Harridge Robert D Knight Peter S Zammit eLife Published 14 November 2016 Crick labsFrancesco Saverio TedescoFull details Skeletal muscle differentiation on a chip shows human donor mesoangioblasts' efficiency in restoring dystrophin in a Duchenne muscular dystrophy model Authors (7) Elena Serena Susi Zatti Alice Zoso Francesca Lo VersoFrancesco Saverio Tedesco Giulio Cossu Nicola Elvassore Stem Cells Translational Medicine Published 1 December 2016 Crick labsFrancesco Saverio TedescoFull details piggyBac transposons expressing full-length human dystrophin enable genetic correction of dystrophic mesoangioblasts Authors (14) Mariana Loperfido Susan Jarmin Sumitava Dastidar Mario Di Matteo Ilaria Perini Marc Moore[...]Francesco Saverio Tedesco George Dickson Maurilio Sampaolesi Thierry VandenDriessche Marinee K Chuah Nucleic Acids Research Published 29 January 2016 Crick labsFrancesco Saverio TedescoFull details Intra-arterial transplantation of HLA-matched donor mesoangioblasts in Duchenne muscular dystrophy Authors (33) Giulio Cossu Stefano C Previtali Sara Napolitano Maria Pia CicaleseFrancesco Saverio Tedesco Francesca Nicastro[...] Chiara Bonini Massimo Venturini Letterio S Politi Yvan Torrente Fabio Ciceri EMBO Molecular Medicine Published 1 December 2015 Crick labsFrancesco Saverio TedescoFull details MAR-mediated dystrophin expression in mesoangioblasts for Duchenne muscular dystrophy cell therapy Authors (8) Ruthger W van Zwieten Stefano Majocchi Pavithra Iyer Yves Dussere Stefania PuttiniFrancesco Saverio Tedesco Giulio Cossu Nicolas Mermod Molecular Biology Published 23 September 2015 Crick labsFrancesco Saverio TedescoFull details Pluripotent stem cells for gene therapy of degenerative muscle diseases Authors (4) Mariana Loperfido Heather B Steele-StallardFrancesco Saverio Tedesco Thierry VandenDriessche Current Gene Therapy Published 1 August 2015 Crick labsFrancesco Saverio TedescoFull details Pagination Current page 1 Page 2 Next page Next Last page Last Share the page Share on Twitter Share on Facebook Share on LinkedIn Share on Email
Investigating the role of dystrophin isoform deficiency in motor function in Duchenne muscular dystrophy Authors (19) Mary Chesshyre Deborah Ridout Yasumasa Hashimoto Yoko Ookubo Silvia Torelli Kate Maresh[...] Mariacristina Scoto Giovanni Baranello Adnan Manzur Yoshitsugu Aoki Francesco Muntoni Journal of Cachexia, Sarcopenia and Muscle Published 1 April 2022 Crick labsFrancesco Saverio TedescoFull details
Dystrophin deficiency affects human astrocyte properties and response to damage Authors (10) Jenny Lange Olivia Gillham Reem Alkharji Simon Eaton Giulia Ferrari Monika Madej Michael FlowerFrancesco Saverio Tedesco Francesco Muntoni Patrizia Ferretti Glia Published 1 March 2022 Crick labsFrancesco Saverio TedescoFull details
The non-muscle ADF/cofilin-1 controls sarcomeric actin filament integrity and force production in striated muscle laminopathies Authors (22) Nicolas Vignier Maria Chatzifrangkeskou Luca Pinton Hugo Wioland Thibaut Marais Mégane Lemaitre[...] Guillaume Romet-Lemonne Howard J WormanFrancesco Saverio Tedesco Antoine Jégou Antoine Muchir Cell Reports Published 24 August 2021 Crick labsFrancesco Saverio TedescoFull details
Generation of two genomic-integration-free DMD iPSC lines with mutations affecting all dystrophin isoforms and potentially amenable to exon-skipping Authors (3) Giulia Ferrari Francesco MuntoniFrancesco Saverio Tedesco Stem Cell Research Published 1 March 2020 Crick labsFrancesco Saverio TedescoFull details
Challenging the "chromatin hypothesis" of cardiac laminopathies with LMNA mutant iPS cells Authors (2) Chiara MozzettaFrancesco Saverio Tedesco The Journal of Cell Biology Published 2 September 2019 Crick labsFrancesco Saverio TedescoFull details
Pericytes in muscular dystrophies Authors (3) Louise Anne MoyleFrancesco Saverio Tedesco Sara Benedetti Advances in Experimental Medicine and Biology Published 31 May 2019 Crick labsFrancesco Saverio TedescoFull details
Stem cell culture conditions and stability: a joint workshop of the PluriMes Consortium and Pluripotent Stem Cell Platform Authors (20) Glyn N Stacey Peter W Andrews Ivana Barbaric Charlotta Boiers Amit Chandra Giulio Cossu[...] Valentin P Shichkin Alison R StaceyFrancesco Saverio Tedesco Oliver Thompson Ravenska Wagey Regenerative Medicine Published 2 April 2019 Crick labsFrancesco Saverio TedescoFull details
Combined Notch and PDGF signaling enhances migration and expression of stem cell markers while inducing perivascular cell features in muscle satellite cells Authors (14) Mattia Francesco Maria Gerli Louise Anne Moyle Sara Benedetti Giulia Ferrari Ekin Ucuncu Martina Ragazzi[...] Pierpaolo Ala Paolo De Coppi Shahragim Tajbakhsh Giulio CossuFrancesco Saverio Tedesco Stem Cell Reports Published 5 March 2019 Crick labsFrancesco Saverio TedescoFull details
Modeling skeletal muscle laminopathies using human induced pluripotent stem cells carrying pathogenic LMNA mutations Authors (7) Heather B Steele-Stallard Luca Pinton Shilpita Sarcar Tanel Ozdemir Sara M Maffioletti Peter S ZammitFrancesco Saverio Tedesco Frontiers in Physiology Published 15 October 2018 Crick labsFrancesco Saverio TedescoFull details
Efficient CRISPR/Cas9-mediated editing of trinucleotide repeat expansion in myotonic dystrophy patient-derived iPS and myogenic cells Authors (23) Sumitava Dastidar Simon Ardui Kshitiz Singh Debanjana Majumdar Nisha Nair Yanfang Fu[...]Francesco Saverio Tedesco Joris R Vermeesch J Keith Joung Marinee K Chuah Thierry VandenDriessche Nucleic Acids Research Published 19 September 2018 Crick labsFrancesco Saverio TedescoFull details
Book review Authors (1)Francesco Saverio Tedesco Neuromuscular Disorders Published 1 March 2018 Crick labsFrancesco Saverio TedescoFull details
Reversible immortalisation enables genetic correction of human muscle progenitors and engineering of next-generation human artificial chromosomes for Duchenne muscular dystrophy Authors (21) Sara Benedetti Narumi Uno Hidetoshi Hoshiya Martina Ragazzi Giulia Ferrari Yasuhiro Kazuki[...] George Dickson Graziella Messina Mitsuo Oshimura Giulio CossuFrancesco Saverio Tedesco EMBO Molecular Medicine Published 1 February 2018 Crick labsFrancesco Saverio TedescoFull details
Enhanced energetic state and protection from oxidative stress in human myoblasts overexpressing BMI1 Authors (12) Silvia Dibenedetto Maria Niklison-Chirou Claudia P Cabrera Matthew Ellis Lesley G Robson Paul Knopp[...] Martina Ragazzi Valentina Di Foggia Michael R Barnes Aleksandar Radunovic Silvia Marino Stem Cell Reports Published 8 August 2017 Crick labsFrancesco Saverio TedescoFull details
Muscle interstitial cells: A brief field guide to non-satellite cell populations in skeletal muscle Authors (3)Francesco Saverio Tedesco Louise A Moyle Eusebio Perdiguero Methods in Molecular Biology Published 1 March 2017 Crick labsFrancesco Saverio TedescoFull details
Ret function in muscle stem cells points to tyrosine kinase inhibitor therapy for facioscapulohumeral muscular dystrophy Authors (9) Louise A Moyle Eric Blanc Oihane Jaka Johanna Prueller Christopher RS BanerjiFrancesco Saverio Tedesco Stephen DR Harridge Robert D Knight Peter S Zammit eLife Published 14 November 2016 Crick labsFrancesco Saverio TedescoFull details
Skeletal muscle differentiation on a chip shows human donor mesoangioblasts' efficiency in restoring dystrophin in a Duchenne muscular dystrophy model Authors (7) Elena Serena Susi Zatti Alice Zoso Francesca Lo VersoFrancesco Saverio Tedesco Giulio Cossu Nicola Elvassore Stem Cells Translational Medicine Published 1 December 2016 Crick labsFrancesco Saverio TedescoFull details
piggyBac transposons expressing full-length human dystrophin enable genetic correction of dystrophic mesoangioblasts Authors (14) Mariana Loperfido Susan Jarmin Sumitava Dastidar Mario Di Matteo Ilaria Perini Marc Moore[...]Francesco Saverio Tedesco George Dickson Maurilio Sampaolesi Thierry VandenDriessche Marinee K Chuah Nucleic Acids Research Published 29 January 2016 Crick labsFrancesco Saverio TedescoFull details
Intra-arterial transplantation of HLA-matched donor mesoangioblasts in Duchenne muscular dystrophy Authors (33) Giulio Cossu Stefano C Previtali Sara Napolitano Maria Pia CicaleseFrancesco Saverio Tedesco Francesca Nicastro[...] Chiara Bonini Massimo Venturini Letterio S Politi Yvan Torrente Fabio Ciceri EMBO Molecular Medicine Published 1 December 2015 Crick labsFrancesco Saverio TedescoFull details
MAR-mediated dystrophin expression in mesoangioblasts for Duchenne muscular dystrophy cell therapy Authors (8) Ruthger W van Zwieten Stefano Majocchi Pavithra Iyer Yves Dussere Stefania PuttiniFrancesco Saverio Tedesco Giulio Cossu Nicolas Mermod Molecular Biology Published 23 September 2015 Crick labsFrancesco Saverio TedescoFull details
Pluripotent stem cells for gene therapy of degenerative muscle diseases Authors (4) Mariana Loperfido Heather B Steele-StallardFrancesco Saverio Tedesco Thierry VandenDriessche Current Gene Therapy Published 1 August 2015 Crick labsFrancesco Saverio TedescoFull details